Noj Noj Hauv PKU Noj Li Cas

Kev noj zaubmov PKU yog qhov tsim nyog rau cov neeg uas muaj mob caj ces hu ua phenylketonuria (PKU). Cov neeg muaj phenylketonuria yog ploj lawm ib qho enzyme uas tso cai rau lub cev hloov cov phenylalanine (ib qho amino acid) rau tyrosine (lwm cov amino acid ). Cov phenylalanine nce thiab ua rau lub hlwb puas tsuaj; yog li txhua tus neeg uas muaj PKU yuav tsum tsis txhob noj cov khoom noj uas muaj protein ntau.

Cov menyuam mos thiab cov menyuam mosliab uas muaj PKU xav tau ib hom mis tshwj xeeb uas tsis muaj phenylalanine.

Nws yog qhov tseem ceeb heev uas cov me nyuam mos, cov me nyuam me, thiab cov me nyuam tsis noj zaub mov muaj protein ntau vim tias lub hlwb tab tom hlob sai heev. Yuav tsum tau noj zaub mov heev. Tag nrho cov khoom noj uas muaj protein ntau yuav tsum tau zam.

Cov khoom noj muaj protein ntau yog:

Cov zaub mov, khoom noj txom ncauj, thiab zaub mov uas tau ua nrog cov khoom noj no yuav tsum tau zam dhau - yog li pizza, ncuav mog qab zib, ncuav qab zib, hamburgers, kub dev, mis nyuj khov, yogurt thiab ntau lwm yam khoom noj. Txawm tias tej yam xws li khob cij thiab qee yam hom cereal muaj peev xwm muaj protein ntau dhau. Aspartame tseem yuav tsum tau zam kom zoo vim tias nws yog ib qho ua ke ntawm aspartic acid thiab phenylalanine.

Cov menyuam yaus thiab cov hluas nrog PKU tuaj yeem noj cov txiv hmab txiv ntoo thiab zaub thiab cov cereals thiab crackers tsawg tsawg vim tias cov khoom noj uas muaj protein ntau tsawg. Cov laus yuav tsum ntes zoo zoo rau cov khoom noj zoo li.

Tab sis, noj zaub mov PKU tsis tshua muaj protein ntau rau kev noj qab nyob zoo, yog li cov menyuam yaus thiab cov laus uas muaj PKU yuav tsum haus cov dej haus tshwj xeeb uas tsis muaj phenylalanine.

Tsis tas li ntawd, kev noj haus no yuav tsum tau ua raws li lub neej, thiab cov kev kuaj ntshav tsis tu ncua kom ceev raws cov phenylalanine qib hauv lub cev.

Puas yog PKU Common?

Raws li National PKU Alliance, li ib ntawm 15,000 tus me nyuam muaj PKU. Cov menyuam mos liab nyob rau hauv Tebchaws Meskas thiab ntau lub tebchaws tau sojntsuam tom qab yug menyuam, thiab yog tias cov menyuam mosliab thiab menyuam yaus ua raws li kev noj haus, lawv lub paj hlwb yuav loj hlob zoo li qub.

Cov neeg laus nrog PKU yuav muaj qeeb me ntsis ntxiv nrog cov protein kom tsawg vim hais tias lub hlwb tau tsim, tiam sis PKU tsis ploj thiab noj ntau dhau phenylalanine tuaj yeem ua teeb meem rau lub siab thiab kev nco.

Qhov chaw:

Maher AK. "Simplified noj zaub mov." Kaum Ib Hlis, Hoboken NJ, Tebchaws USA: Wiley-Blackwell Publishing, Kaum Hlis 2011.

Merck Manual - Professional Version. "Amino Acid thiab Organic Acid Metabolism Disorders." http://www.merckmanuals.com/ profofessional/pediatrics/inherited-disorders-of-metabolism/overview-of-amino-acid-and-organic-acid-metabolism-disorders.

National Alliance Alliance. "Phenylketonuria Qhov tseeb rau tsev kawm ntawv cov kws qhia ntawv thiab cov neeg ua haujlwm." http://www.npkua.org/Portals/0/PKU_schoolfacts.pdf .